A prenatally diagnosed case of sirenomelia with dextrocardia and omphalocele.
نویسندگان
چکیده
OBJECTIVE Sirenomelia (Mermaid syndrome) is a rare anomaly of caudal region of the body, presented with fusion of the lower limbs. Genito-urinary, gastro-intestinal, neural tube and vertebral anomalies are found in most cases. METHODS We present a case of sirenomelia diagnosed in the first tri-mester, associated with dextrocardia, and omphalocele CONCLUSION First trimester diagnosis of sirenomielia is possible and early diagnosis gives the parents the option of early pregnancy termination.
منابع مشابه
Omphalocele with dextrotardia-A rare association.
Omphalocele is frequently associated with many other congenital malformations. In cardiac anomalies, association of omphalocele with dextrocardia has been rarely noticed before. We present here a child with dextrocardia and omphalocele alongwith a brief review of the literature on this rare association.
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ورودعنوان ژورنال:
- Journal of prenatal medicine
دوره 3 3 شماره
صفحات -
تاریخ انتشار 2009